Monday, February 18, 2013

Sickle-Cell Selection


Sickle-cell disease (SCD) is a genetic blood disorder in red blood cells. The disease is autosomal recessive, and it turns the erythrocytes into a sickle shape instead of the normal rod-shaped. The new shape is caused by a mutation in a hemoglobin gene. People with SCD can have a variety of complications ranging from anemia to a stroke. The interesting part about sickle-cell disease is its prevalence in sub-tropical sub-Saharan regions. These regions are also known to have high cases of malaria, which is a disease caused by protists of the genus Plasmodium. People with the autosomal recessive disease, or people who carry the sickle cell trait, are known to be resistant to the Plasmodium falciparum. Therefore, natural selection takes place in these areas with high cases of malaria, and the sickle cell trait gets passed on.

Researchers have studied the role of the sickle cell hemoglobin (HbS) in sub-Saharan Africa where “moderate-to-intense malaria transmission” is present (Terlouw). A lot of the children there tended to have the sickle cell trait, which is why researchers decided to study the effect of a particular antimalarial drug on young children. More specifically, they were trying to determine the effect of sulfadoxine-pyrimethamine to clear P. falciparum parasites. They found that those children with the sickle cell trait reacted to the drug a lot better than those without the trait (Terlouw). Natural selection acts again. The sickle cell trait outcompeted the dominant trait when trying to survive in the presence of the drug. This cannot be due to random selection because the sickle cell trait remained in high quantity among the children, which further demonstrated that natural selection took place. If we continue to make drugs to cure diseases, it is important that we take evolution into account because it will give us a better understanding of how to fight off these different diseases such as malaria. 

Word Count: 313 

Source

Feiko O. ter Kuile, et al. "Increased Efficacy Of Sulfadoxine-Pyrimethamine In The Treatment Of Uncomplicated Falciparum Malaria Among Children With Sickle Cell Trait In Western Kenya." The Journal Of Infectious Diseases 11 (2002): 1661. JSTOR Life Sciences. Web. 18 Feb. 2013.

Alyssa Thomas 

6 comments:

  1. The children with the sickle cell allele reacted to the antimalarial drug "a lot better"...so what does this mean for the children with the allele for normal shaped blood cells? selection implies differential survival, but I hope this doesn't mean that the children without the sickle cell allele succumbed to the antimalarial drug at a higher rate...in which case, it's not a very good drug and should be re-evaluated

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  2. Can you define "a lot better" in regards to how the children with a sickle cell trait react to the medication? It would be nice to see how well they responded and how this response held its strength with time.
    -Mary Morales

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  3. Did the scientists have any theories as to why sickle cell trait kids responded better to the drugs? Additionally, how do they isolate efficacy of the drug from inherent resistance of sickle cell trait patients to malaria?
    -Tom Xia

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  4. I would not call this a natural selection. The presence of drug actually makes it an artificial selection. I am not even sure if the children with sickle cell will necessarily "outcompete the dominant" because they still suffer from sickle cell anemia. Also remember in class we discuss about how the presence of sickle cell could be due to the heterozygote advantage to malaria, which increases the number of gene carriers.

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  5. Isn't having the heterozygous sickle cell trait the most advantageous in that it fights malaria without them actually having the full sickle cell disease? How does the heterozygous rate compare to the sickle cell trait when it comes to malaria?

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  6. I am a bit confused as to the results of this drug treatment. If I understand correctly, the drug treatment showed better efficacy in those children who carried the sickle cell trait (heterozygous) than those who did not have the trait or disease at all (homogeneous dominant). Though, the drug might have shown better results for those who were carriers, I don't believe that this really has to do with "out-competing" those who were homogeneous dominant. As stated previously stated by Peter and Briona, I would more attribute this phenomenon to heterozygous advantage. Additionally, if the frequency of the sickle cell trait still remained quite high after use of the drug, for how many generations was the drug tested? If it was to provide some sort of advantage for natural selection, then wouldn't the results of the drug have to be shown over many generations in humans?

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